A case of Paget's disease with facial palsy Paget's disease with facial palsy

Abstract

Paget's disease of bone is the second most common metabolic bone disease in European countries, although Paget's disease is uncommon in Japan. Paget's disease can affect one or multiple bones in the systemic skeleton, including the temporal bone. Paget's disease of the temporal bone is often associated with a mixed hearing loss or hemifacial spasm or expansion of head circumference. But the facial nerve palsy has rarely been reported.
We reported the case of a 52-year-old woman with left facial palsy and auditory disturbance due to Paget's disease at the left temporal bone.
We had chosen steroids treatment at first, and bisphosphonate was given, but her facial palsy was not improved. Three months later, the patient underwent operation of the facial nerve decompression and meatoplasty because the level of ENoG was deteriorated. The facial nerve was decompressed from bone and swelling. After the operation, her severe facial palsy and auditory disturbance were recovered.
Paget's disease at the temporal bone rarely accompanied with facial nerve palsy. We review the literature and discuss clinical features and management of this rare case.