Abstract
We reported a case of congenital cholesteatoma localized in the mastoid cavity.
A right sided conductive hearing loss was found in a patient during the preschool medical checkup and later the diagnosis was confirmed by computed tomography. The causes of conductive hearing loss were multiple ossicular chain anomalies, such as absence of the incus and the anterior crus of stapes, and displacement of the posterior crus of stapes. We performed tympanoplasty type IVi.
Most cases of congenital cholesteatomas are less likely to be diagnosed as the ossicular chain anomaly, but the present case was showing the ossicular chain anomaly. Because there was no anatomical relation between the location of cholesteatoma and lesion of ossicular chain.
