A case report of multiple congenital cholesteatomas

Abstract

We report a case of multiple congenital cholesteatomas. A 7-year-old girl presented with suggested right-ear hearing loss during a medical checkup in her elementary school. On examination, a white lesion was observed through the intact eardrum. A two-staged operation was performed. The initial procedure revealed 11 cholesteatomas between the posterior tympanum and the mastoid. Two residual cholesteatomas were extracted and a tympanoplasty type IVc performed during the second-look procedure. The post-operative condition of the eardrum was satisfactory; however, long-term follow-up is required.