1991 Volume 1 Issue 2 Pages 29-33
Three cases of van der Hoeve syndrome were reported. Two cases showed a conductive or mixed deafness which resembled to those of otosclerosis. The operative findings revealed the pathophysiology of deafness to be fixation of the stapedial footplate in one case and the combination of fixation of the footplate and fibrous change of the crura in another case. The third case showed profound mixed deafness. The pathophysiology of this case was considered to be similar to that of cochlear otosclerosis by the findings of high resolution CT scan. The diagnostic and therapeutic problems of this syndrome were discussed with a review of literature.
