Congenital cholesteatoma in the tympanic cavity accompanied with congenital ossicular anomaly

Abstract

In a 11-year-old male patient with left hearing loss, otoscopic examination revealed the intact tympanic membrane, and the left ossicular anomaly was suspected by preoperative examinations. During surgery, the long process of the incus and the superstructure of the stapes were not recognized and two different types of congenital cholesteatomas (an open type and a closed type) were found in the middle ear cavity.
Coexistance of open and closed type cholesteatomas in the middle ear was very rare. We discussed the origin of the open type congenital cholesteatoma and embryological problems.