A case of intraductal papillary mucinous tumor (IPMT) with extrahepatic cholangiocarcinoma

Abstract

We report on a case of intraductal papillary mucinous tumor (IPMT) with extrahepatic cholangiocarcinoma. A 50-year old man was admitted to our hospital with obstructive jaundice. Ultrasonography and computed tomography (CT) of the abdomen revealed a tumor in the common bile duct, which caused dilation of the upstream bile duct, and a cystic lesion in the head of the pancreas. Endoscopic retrograde cholangiopancreatography (ERCP) was performed. The papilla resembled a“fish-eye”, with mucus extruding from the orifice. A filling defect in the common bile duct and a segmentally dilated pancreatic duct in the pancreatic head were seen. He underwent pancreaticoduodenectomy. Histological testing of the specimen revealed cholangiocarcinoma of the common bile duct and IPMT in the head of the pancreas. IPMT is a rare cystic neoplasm of the pancreas. The majority of patients with IPMT do not have invasive cancer, and usually have a prolonged course without the development of cancer. However, concomitant malignancies of other organs occur in association with IPMT. Careful follow-up is necessary for patients with IPMT.