2010 Volume 21 Issue 4 Pages 345-350
Klippel-Trenaunay syndrome (KTS) is a congenital disorder, which is characterized by naevus, venous abnormalities, and deformities of soft tissue and bone in the affected extremity.
A 52-year-old male complained of severe dullness and presented with extensive varicose veins and hypertrophy of the right lower extremity. His right lower extremity also showed cutaneous port wine stains. Preoperatively, his right lower extremity was evaluated by ultrasonography to determine patency of the deep veins and reflux of superficial veins. Surgery for the varicose veins was performed under local anesthesia (ligation of the greater & small saphenous veins, lateral marginal vein and incompetent perforator). Two months later, additional venous ligation and sclerotherapy were performed. Without any complications, he was significantly relieved from the symptoms due to venous stasis.
Surgical management based on the ultrasonographic findings should be considered as one of the strategies to treat the KTS patients with severe symptoms.
