2022 Volume 13 Issue 1 Pages 54-58
An 8-year-old boy with a 3-week history of spiking fever and arthritis visited to the previous hospital. His blood tests revealed liver dysfunction and hyperferritinemia (ferritin 2,043 ng/mL), and he was referred to our hospital. On the first visit to our hospital, he presented a unique rash, so-called prurigo pigmentosa-like eruption, in addition to the typical evanescent rashes on his trunk. A diagnosis of s-JIA was made. After prednisolone administration was started, his symptoms, including the fever, arthralgias, and skin rash, improved. Various skin eruptions appear in adult-onset Still’s disease (AOSD), the adult form of s-JIA. However, those atypical eruptions rarely occur in s-JIA. The presence of the typical evanescent rash is important to establish the diagnosis. We should be aware that prurigo pigmentosa-like eruptions could appear in children with s-JIA and AOSD.
