Abstract
A 77-year-old female with Von Recklinghausen's disease who presented with jaundice and fever was found to have carcinoma of the papillary region in the duodenum on barium meal examination, CT scan, ultrasound and percutaneous transhepatic cholangiogram. At laparotomy, multiple leiomyomas were discovered on the serosal surface of the jejunum. Only three cases of primary duodenal carcinoma with small bowel leiomyomas in a patient with Von Recklinghausen's disease have been reported in the literature.
