A CASE OF NEUROFIBROMATOSIS ACCOMPANIED BY PHEOCHROMOCYTOMA AND MULTIPLE SMALL INTESTINAL LEIOMYOMAS

Abstract

Pheochomocytoma is not a common disease. Neurofibromatosis means any of various clinically and genetically heterogenous disordes associated with multiple neurofibromas, especially neuroendocrine neoplasma. Among these neoplasms pheochromocytoma is most common.
A recent experience with a case of neurofibromatosis associated with pheochromocytoma and multiple small intestinal leiomyomas in a 59-year-old is reported. The patient was diagnosed as neurofibromatosis fourty years before admission. Peochoromocytoma and multiple small intestinal leiomyomas were found during operation.
We must consider a possible associon of pheochoromocytoma when we see the patient with neurofibromatosis complaining of hypertension. There are a few reports of duodenal carcinoid found in such a patient, so upper gastrointestinal examination is also indispendable before operation.