A CASE OF KARTAGENER'S SYNDROME WITH SEVERE HEMOPTYSIS

Abstract

A 33-year-old woman was emergently admitted to the ICU because of severe hemoptysis. There was a history of chronic sinusitis. Observed by bronchofiberscopic examination. Chest X-ray film showed dextrocardia and infiltration shadow in both lower lung fields. Consecutively, bronchogram, bronchial arteriogram, pulmonary perfusion scanning and inhalation scanning examination revealed that the right lower lobe was ectatic and dysfunctional. Surgical treatment was performed at this area. The cilia of this bronchial mucous membrane showed missing and irregular arrengement of the microtubles and a defect of dynein arma by electron microscopic examination. This patient was diagnosed as Kartagener's syndrome, which is now considered as a type of primary ciliary dyskinesia.