Abstract
A case of malignant small cell tumor of the thoraco-pulmonary region, so called Askin tumor, in a three year-old female complaining fever is described.
In the chest plain roentrenogram and pulmonary CT scan, a spindle shaped chest wall mass situated on the right 5th rib was disclosed. The rib destructed. Ewing sarcoma or osteosarcoma was suspected. The chest wall resection with the 5th to 7th ribs, and the partial resection of the pulmonary segment 4 were performed. The tumor was elastic soft and 80×30×25 mm in size, a grayish-white appearance. The ribs, lung, and pleura were involved. Pathologically, the tumor was diagnosed as Askin tumor.
Askin tumor is uncommon in infants and the prognosis is generally so dismal. Here the important of multidisplinary treatments as well as early diagnosis and operation is emphasized.
