Abstract
Perineal liposarcoma is exceedingly rare. A 72-year-old man was seen at the hospital because of a perineal tumor. Diagnostic imagings indicated a pararectal tumor and an operation was carried out. Histologically it was well-differentiated liposarcoma of the sclerosing type. This was the first case in Japan. Five other reports of retrovesical or perineal liposarcoma was culled from the literature in foreign countries. A total of cases of liposarcoma including the present case reported between 1904 and 1988, are also reviewed here.