A CASE OF RETROPERITONEAL MUCINOUS CYSTADENOCARCINOMA

Abstract

The great majority of tumors arising in the retroperitoneum are non-epithelial tumor. Primary retroperitoneal mucinous cystadenocarcinoma is very rare. We present such a rare case with some notes on 23 cases reported in the Japanese literature. A 39-year-old woman was admitted to the hospital because of distention and tenderness of the right lower quadrant of the abdomen.
Abdominal imagings revealed a giant cystic mass 20×18×15cm in size and an intracystic tumor 2cm in diameter. Abdominal angiography revealed displacement of the left lower abdominal vessel. Barium enema study showed no abnormal findings other than oppression image. At laparotomy, a large cystic tumor was found in the leftlateral abdominal region which showed extramural pressure to the colon. Macroscopic photograph of resected specimen showed simple large cyst with protruding papillary tumor inside of the cyst and the inner space was filled with mucinous fluid. Histologically, it was mucinous cystadenocarcinoma. The mucinous fluid and cystic wall were CA19-9 positive on immunohistochemical studies.
The Patients is living and has been free from recurrence for 2 years after the operation. Since no abnormalities in other organs have been seen, we think that the tumor was primary retroperitoneal mucinous cystadenocarcinoma.