A CASE OF MULTIPLE PILOMATRICOMA

Abstract

A 12-year-old Japanese girl presented with a subcutoneous tumor on her back. Since 6 years old when she had a pilomatrixoma on her right arm, She had had a total of six pilomatrixomas on the left shoulder, left cheek, right back, left back and neck. All these lesions were surgically removed and diagnosed as pilomatricoma on histological examinations. This time, the tumor on her back was also resected and proved to be the seventh pilomatricoma.
Pilomatricoma is a benign subcutaneus tumor which frequently involves the head, neck and upper extremities in young women and usually occurs as a solitary legion. Multiple pilomatricoma, mostly 2 or 3 incidents, has been reported to occur in approximately 10% of all cases. However, a case of 7 tumors like this case is rare. The associations of multiple pilomatricoma and myotonic dystrophy have been occasionally seen in the literature. Although pilomatricoma is generally considered benign tumor, it car gradually in crease in size if it is let alone and there are a few reports of malignant pilomatricoma. It is suggested that pilomatricoma should be removed as soon as possible.