Abstract
A 43-year-old woman with a right vulvar mass was found in computed tomography (CT) and magnetic resonance imaging (MRI) to have a tumor of the right vulva extending into the pelvis. This tumor was resected through separate abdominal and perineal incisions, with a histological diagnosis of aggressive angiomyxoma. This is extremely rare, with only 16, including our case, reported in Japan to date. The excised tumor was, at 30×22×8cm, the largest among those reported in Japan. This lesion usually occurs in the perineum or vulva of relatively young women. This case is reported along with a review of other cases reported in Japan and other literature.
