Abstract
We report a rare case of congenital choledochal cyst with intestinal malrotation.
A 32-year-old woman was admitted to the hospital because of upper abdominal pain and back pain. Abdominal ultrasonography revealed a cystic mass in the hepatic hilum. Abdominal CT scan showed a giant cystic mass near the common bile duct. Upper gastrointestinal series showed the displacement of the horizontal portion of the duodenum and the entire small intestine to the right. The entire large intestine was located on the left, yielding a diagnosis of nonrotation by a barium enema study. Pancreaticobiliary maljunction was uncertain by endoscopic retrograde cholangio-pancreatography (ERCP). After percutaneous intrahepatic drainage under echo guidance of the cystic lesion, we performed an excision of the choledochal cyst with reconstruction of the biliary tract because of a suspicion of malignancy on cytology. Postoperative pathological examinations showed no evidence of malignancy.
