1981 Volume 10 Pages 59-63
9 cases of adult type of Moyamoya disease were reviewed, all of which started with intracerebral hemorrhage.
During the past 5 years, we experienced 13 cases of adult Moyamoya disease, 9 of which began with intracerebral hemorrhage and the other 2 cases started with subarachnoid hemorrhage. The age of onset ranged from 22 to 55 years old. There were 7 females and 2 males.
As the initial symptoms headache and vomiting were seen in all 9 cases and the disturbance of consciousness was noted in 8 cases. As the treatment, simple evacuation of hematoma was done in a case and 4 cases were treated conservatively. Surgical extra- and intracranial arterial bypass was performed in 4 cases after absorption of hematoma. The prognosis was generally poor. Only 2 cases could return to useful life and 4 cases subsequently died. The location of intracerebral hematoma on CT scan was mostly in paraventricular region, such as the head of caudate nucleus, thalamus and putamen. The hematoma had been perforated into ventricles in all cases, the size of which was larger than original intracerebral hematoma in 5 cases.
