Cochlear Implantations for Children with Congenital Inner Ear Malformation

Abstract

From April 1996 through November 2003 we had four cases of cochlear implant for children with congenital inner ear malformation. We reported on each operation technique used and the postoperative hearing level of these four cases. Three these cases had the Mondini deformity. The other had a common cavity deformity. CSF gusher in cochleostomy occurred in one of the three Mondini deformity cases. It is important to bear in mind abnormalities in the intratympanic course of the facial nerve, constriction of internal auditory meatus, cochlear nerve defect, CSF gusher in cochleostomy and meningitis after cochlear implantation, when the operation is being performed on children with inner ear malformation.