Abstract
The patient was a 41-year old male. One year ago a red nodule developed on the ulnar side of the DIP of the right ring finger and became enlarged, reaching a diameter of 12mm and a height of 5mm. Based on the histopathologic HE and CD34 immune staining, a dermatofibrosarcoma protuberans was diagnosed. Imaging findings did not reveal any distant metastases. Following the wish of the patient, a total resection with a horizontal margin of 5mm and a vertical margin reaching down to the tendon followed by a skin graft was performed. The patient has now been free from local recurrence and metastasis for five years after surgery. In the past 46 years only a rare 7 cases with this condition have been reported.[Skin Cancer (Japan) 2009 ; 24 : 309-313]