Abstract
Syringomatous carcinoma (SC) is a rare malignant appendageal tumour. Subsequently neoplasms in the same category with different degrees of differentiation were reported with various designations, such as eccrine epithelioma, basal cell tumor with eccrine differentiation, syringoid eccrine carcinoma, sclerosing sweat duct syringomatous carcinoma, sweat gland carcinoma with syringomatous features, and microcystic adnexal carcinoma. In 1990, Abenoza and Ackerman proposed the term ‘syringomatous carcinoma’ for the various neoplasms. Since then, 16 cases have been reported in Japan. We present the case of a 69-year-old woman with SC on the dorsum of her left middle finger proximal interphalangeal joint, in whom local excision of the tumor was performed. SC is characterized histopathologically by asymmetrical and deep invasion of tumour cells into the subcutaneous tissue and multiple small nests that resemble those of a syringoma, and duct formation.[Skin Cancer (Japan) 2012 ; 27 : 48-51]