Abstract
A 63-year-old man noticed an asymptomatic nodule on the right cheek, which had gradually grown to measure 12 mm in diameter since two year ago. The tumor was diagnosed as a primary mucinous carcinoma of the skin (PMCS) by a skin biopsy and systemic examinations. Ninety-three cases of PMCS have been reported in Japan since 12 years ago. Eighty-three percent of the PMCS presented on the craniofacial region. PMCS is one of the rare malignant skin tumors. However, there are many kinds of skin tumor which mimic PMCS. We should consider PMCS as one of the differential diseases that occur on the craniofacial region.[Skin Cancer (Japan) 2013 ; 28 : 340-343]