2022 Volume 37 Issue 3 Pages 187-191
A 37－year－old man noticed a small nodule on his right forearm 7 months before his first visit. The nodule showed enlargement, and he observed new nodules on his forearm and hand. Histopathological evaluation of an excisional biopsy specimen obtained from a nodule revealed findings of epithelioid sarcoma. All nodules were excised with 2－cm margins, and we performed prophylactic lymph node dissection. The surgical margin was negative ; however, we detected micrometastasis in one of the dissected lymph nodes. We administered 3 courses of doxorubicin and ifosfamide as postoperative adjuvant therapy. Epithelioid sarcoma is characterized by not only frequent local recurrence but also lymphatic spread, which is usually uncommon among sarcomas. An epithelioid sarcoma is an extremely rare tumor, and standardized therapy is unavailable ; therefore, large－scale retrospective studies are warranted to gain deeper insight into this malignancy.[Skin Cancer (Japan) 2022 ; 37 : 187－191]
