Abstract
We report a case of 74-year-old woman who developed leukoderma of the vulva for a half year. There was no history of similar skin lesions in her family members. She was treated with topical steroid ointment but did not get well. On physical examination she had keratinized leukoderma on the clitoris and the labia minora. The histopathological examination showed acantholysis, dyskeratosis and clefting in epidermis similar to that seen in Hailey-Hailey disease and also showed epidermolytic hyperkeratosis.
This case was thought to be a case of acantholytic dermatosis localized to the vulvocrural area reported by Cooper and Chorzelski with epidermolytic hyperkeratosis.
The erupution cleared almost 1 month after the initiation of treatment with systemic etretinate and topical steroid ointment.
