Congenital hemihypertrophy with complained of difficult mastication: Report of a case and review of the literature

Abstract

Hemihypertrophy is a rare disorder in which there is enlargement of some or all parts of the body. The first case was recorded by Wagner in 1839. Recently, it has been interested in children with congenital hemihypertrophy who are usually at a higher risk for developing intra-abdominal malignant tumor and other abnormalities.
This case, a 5 year old boy with hemihypertrophy complained of mastication difficulty, is reported.
He was noted to have excessive overgrowth on the left side at birth.
He had some abnormalities; mental deficiency, nevi, epilepsy, cryptorchidism, increased hairiness on involved side, expanded cerbral hemisphere on involved side, abnormality of electroencephalogram and otorrhea. There was a 32×18mm excrescence of lingual gingiva of the left lower jaw in the molar teeth region.
Other dental points of view of the oral condition were as follows;
The left side of the tongue was enlarged and the fungiform papillae were grossly hypertrophic. There was a fusion of the erupted primary teeth in the right lower jaw. There wer esome congenital missing teeth. There were premature eruption and development of the teeth in the left side.
We excised the excrescence of lingual gingiva of the left lower jaw in the molar teeth region, to improve mastication.
He has had an uneventful course for about one year and three months to date, and no recurrence has been noted.