A case of solid pseudopapillary tumor of the pancreas with pancreas divisum

Abstract

A 30-year-old woman was found to have a pancreatic tumor. Abdominal ultrasonography showed a solid tumor without cystic component lesion in the head of pancreas that was 2cm in the diameter. Dynamic computed tomography showed that the tumor was a low density lesion and slightly enhanced in the portal phase. Positron emission computed tomography showed a high uptake tumor with a maximum index of 8.0. Endoscopic retrograde pancreatography showed no communication between the ventral and dorsal pancreatic ducts, indicating that pancreas divisum was present. The patient underwent a pancreaticoduodenectomy. Immunohistochemical analysis demonstrated that the tumor cells were positive for synaptophysin and CD10 but negative for chromogranin A and CD56. The tumor was diagnosed as a solid pseudopapillary tumor of the pancreas. A search of PubMed turned up only one report of concomitant solid pseudopapillary tumor and pancreas divisum. Solid pseudopapillary tumors of the pancreas with pancreas divisum are extremely rare.