Abstract
Extrahepatic bile duct anomalies are not so rare and care should be taken in operation for such anomalies. We report a case of gallbladder cancer associated with pancreaticobiliary maljunction with long accessory hepatic duct. A 72-year-old man was admitted to our hospital, he complained of right hypochondralgia. Ultrasonography revealed tumor of gallbladder. ERCP, CT and abdominal angiography showed gallbladder cancer associated with pancreaticobiliary maljunction. A long accessory hepatic duct was seen on ERCP. We recognized this bile duct arising from left caudate lobe and draining into the lower bile duct intraoperatively. Attention must be paid to the presence of unexpected biliary anomalies for the operation of pancreaticobiliary maljunction or bile duct dilatation. In dissection of hepatoduodenal ligament, we have to pay attention to the presence of accessory hepatic duct like this case.