Allergology International
Online ISSN : 1440-1592
Print ISSN : 1323-8930
ISSN-L : 1323-8930
A Case of Juvenile Dermatomyositis Manifesting Inflammatory Epidermal Nevus-Like Skin Lesions: Unrecognized Cutaneous Manifestation of Blaschkitis?
Yuji TakahashiHiroyuki MurotaMasahito TarutaniShigetoshi SanoTakeshi OkinagaKoji TominagaToshie YanoIchiro Katayama
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2010 Volume 59 Issue 4 Pages 425-428


Background: Juvenile dermatomyositis is potentially life threatening rare autoimmune illness that mainly affects muscle and skin. Cutaneous features are useful in establishing the diagnosis of this disease.
Case Summary: We report an 8-year-old male juvenile dermatomyositis who presented epidermal nevus like-lesions on the back of the right thigh. Characteristic cutaneous changes such as Gottron's papules of the hand, heliotrope rash of the eyelids, and poikiloderma-like lesions on the back were observed. Diagnosis of juvenile dermatomyositis was made by positive muscle biopsy and magnetic resonance imaging findings and typical cutaneous manifestations. However, epidermal nevus-like skin lesions, an acquired inflammatory dermatosis that follows Blaschko lines, seen in this case have been rarely reported in the literatures.
Discussion: We would like to report this case and discuss about the significance and pathogenesis of this rare cutaneous manifestation like Blaschkitis in juvenile dermatomyositis.

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© 2010 by Japanese Society of Allergology
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