Pinhole Descending Aortic Rupture with Systemic Sclerosis and Dermatomyositis: A Case Report

Abstract

Thoracic descending aortic perforation with overlap syndrome (systemic sclerosis and dermatomyositis) is a rare, unreported vascular pathology. We describe the case of a 75-year-old woman who presented with chest tightness, back pain, and dyspnea. Computed tomography revealed a pinhole rupture in the descending aorta. The patient underwent a thoracic endovascular aortic repair and left chest drainage. Her postoperative course was uneventful.