1993 Volume 35 Issue 2 Pages 372-377_1
Laparoscopical and histological findings of the liver were examined in two patients with both congenital hepatic fibrosis and Caroli disease. Patient 1 was 25 years old female, and was referred to our department because of pancytepenia which was found at her first delivery. Patient 2 was 41 years old female, and visited our hospital because of fever and right hypochondralgia. Cholagiography showed multiple cystic dilatations of intrahepatic bile duct which indicated Caroli disease in both patient. Histological examination revealed wide fibrosis of portal area, increased number of dilated bile duct and decreased number of portal vein in both patient, indicating congenital hepatic fibrosis. Wide and discrete whitish marking which reflect marked fibrosis of portal area was observed in reticular or tree branch pattern laparoscopically. This whitish marking was supposed to be a charac-teristic laparoscopical finding in patients with congenital hepatic fibrosis.
