A Case of Malignant Hemangiopericytoma of Mediastinal Origin

Abstract

A 27-year-old male was admitted to our hospital with recurrence of left intrathoracic tumor. Emergency left thoracotomy and tumor extirpation was performed, and histological examination revealed malignant hemangiopericytoma. Repeated extirpation of tumors, left pneumonectomy accompanied by partial resection of the pericardium and diaphragm, and also resection of the left lateral chest wall were performed successively for the recurrent lesion. Neither chemotherapy using a combination of Cisplatin, Doxorubicin hydrochloride and Cyclophosphamide nor Linac irradiation yielded effective control of the tumor growth. He died of disseminated metastases in the right lung and disseminated intravascular coagulation syndrome nine months after the first operation.
Concluding from the operative findings that the mass was continuous with the mediastinal pleura and since no intrapulmonary lesion was present, the tumor seemed to be of mediastinal origin.