Myocardial Involvement in Benign Duchenne Type of Progressive Muscular Dystrophy

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Two cases of benign Duchenne type of progressive muscular dystrophy with myocardial involvement were presented. In one case, congestive heart failure was the predominant clinical feature and severe impairment of the left ventricular function was demonstrated by hemodynamic and cineangiocardiographic studies. Analysis of the cineangiocardiogram demonstrated a systolic expansion of the posterolateral portion of the left ventricular wall in both cases, which corresponded to the site of severe myocardial damage of the left ventricle in one autopsied case. A possible relationship between the site of myocardial damage and electrocardiographic and vectorcardiographic abnormalities was also discussed.