A Case of Constrictive Endocardial Sclerosis Accompanied with Congenital Lutembacher's Syndrome

抄録

A 4-month-old boy with congenital Lutembacher's syndrome was reported. In the underdeveloped left ventricle, characteristic constrictive endocardial sclerosis, which contained very few elastic fibers and showed nodular myxomatous feature with fibrosis, was found. The characteristic endocardial involvement may be called as "constrictive endocardial sclerosis."