Abstract
A world-oldest necropsy case of the isolated levocardia with situs inversus abdominalis and polysplenia was presented. The case was 75-year-old female, who died of bronchopneumonia and cerebral thrombosis. The heart showed rather symmetrical architecture, that is, (1) almost same level of mitral and tricuspid ring and therefore absence of atrial part of the pars membranacea, (2) an anomalous muscle bundle in the left ventricle simulating the crista supraventricularis and (3) symmetrical course of the conduction system in the central fibrous body.
Thirty-one cases with combination of levocardia and situs inversus abdominalis in Japanese literatures were reviewed. Only 2 of them had grossly normal hearts and the others had major anomalies incompatible to long survival.