抄録
Langerhans cell histiocytosis (LCH), a monoclonal disease of histiocytes, may involve several organ systems but rarely involves the maxillary sinus as a primary site. This report presents an extremely rare case of LCH of the maxillary jaw in an 11-month-old girl. An incisional biopsy for a maxillary lesion was performed, and a histopathological diagnosis of LCH was established. The histopathological examination revealed the proliferation of histiocytes with an infiltration of eosinophils. Histiocytes were positive for S-100 and CD68(KPI). The patient subsequently underwent chemotherapy with the resolution of LCH in the maxillary jaw, and has continued to show partial response as of 1 year after chemotherapy.
