Internal Medicine
Online ISSN : 1349-7235
Print ISSN : 0918-2918
ISSN-L : 0918-2918
Neurological Diseases
Advanced Hirayama Disease with Successful Improvement of Activities of Daily Living by Operative Reconstruction
Susumu CHIBAKazumi YONEKURAMichio NONAKATomihiro IMAIHiroyuki MATUMOTOTakuro WADA
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JOURNALS OPEN ACCESS

2004 Volume 43 Issue 1 Pages 79-81

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Abstract

Juvenile muscular atrophy of the distal upper extremity (Hirayama disease) is a benign and non-progressive motor neuron disease. Application of a cervical collar is believed to prevent progression of symptoms in the early stages, but there is no effective therapy for the advanced disease. We found that tendon transfer improved the activities of daily living (ADL) of a patient with advanced Hirayama disease. An operative reconstruction can be valuable, even in patients with Hirayama disease who have developed impaired ADL due to extensive intrinsic hand muscle atrophy.

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© 2004 by The Japanese Society of Internal Medicine
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