A Case of Systemic Amyloid A Amyloidosis Secondary to Xanthogranulomatous Pyelonephritis

Masato Habuka; Mizusa Nishikiori; Chihiro Oikawa; Megumi Takahashi; Yuichi Sakamaki; Asa Ogawa; Norio Miyajima; Yasuhiko Tanabe; Keiichi Honma; Kunihiko Wakaki; Suguru Yamamoto; Ichiei Narita

doi:10.2169/internalmedicine.1806-23

This article has now been updated. Please use the final version.

A Case of Systemic Amyloid A Amyloidosis Secondary to Xanthogranulomatous Pyelonephritis

Masato Habuka, Mizusa Nishikiori, Chihiro Oikawa, Megumi Takahashi, Yuichi Sakamaki, Asa Ogawa, Norio Miyajima, Yasuhiko Tanabe, Keiichi Honma, Kunihiko Wakaki, Suguru Yamamoto, Ichiei Narita

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Keywords: systemic AA amyloidosis, xanthogranulomatous pyelonephritis, serum amyloid A

JOURNAL OPEN ACCESS Advance online publication

Article ID: 1806-23

DOI https://doi.org/10.2169/internalmedicine.1806-23

The final version of this article is now available: Vol. 63 (2024), No. 4 pp. 593-599

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Abstract

The combination of systemic amyloid A (AA) amyloidosis and xanthogranulomatous pyelonephritis (XGP) resulting from a chronic urinary tract infection is extremely rare. We herein report a case of systemic AA amyloidosis secondary to XGP for which clinical remission developed after nephrectomy. To our knowledge, this is the first case report describing the clinical improvement of systemic AA amyloidosis secondary XGP after nephrectomy in Japan. Clinicians should be aware of this uncommon combination and search for amyloid depositions in cases of XGP.

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