IgG4-related Disease Involving the Cardiovascular System: an Intracardiac Mass and a Mass Lesion Surrounding a Coronary Artery

Ryotaro Maeda; Daisuke Naito; Atsuo Adachi; Hirokazu Shiraishi; Takashi Sakamoto; Satoaki Matoba

doi:10.2169/internalmedicine.2509-18

This article has now been updated. Please use the final version.

IgG4-related Disease Involving the Cardiovascular System: an Intracardiac Mass and a Mass Lesion Surrounding a Coronary Artery

Ryotaro Maeda, Daisuke Naito, Atsuo Adachi, Hirokazu Shiraishi, Takashi Sakamoto, Satoaki Matoba

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Keywords: IgG4-related disease, intracardiac mass, intracardiac echo, computed tomography angiography, Fluorodeoxyglucose positron emission tomography

JOURNAL OPEN ACCESS Advance online publication

Article ID: 2509-18

DOI https://doi.org/10.2169/internalmedicine.2509-18

The final version of this article is now available: Vol. 58 (2019), No. 16 pp. 2363-2366

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Abstract

A 61-year-old Japanese man with IgG4-related autoimmune pancreatitis developed a mass in the right atrium (RA) and a mass lesion surrounding the left anterior descending coronary artery. We performed an intracardiac echo catheter-guided percutaneous biopsy of the RA mass, and histologically diagnosed it as IgG4-related disease. Oral corticosteroid therapy gradually downsized the mass lesions. We encountered a very rare case with mass lesions in the cardiovascular system of the IgG4-related disease that were able to be diagnosed using an intracardiac echo-guided biopsy.

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