A Case of an Splenic Artery Aneurysm and Focal Nodular Hyperplasia Associated with an Abdominal Vascular Abnormality of Hereditary Hemorrhagic Telangiectasia

Satoru Hagiwara; Koichi Nakagawa; Yoriaki Komeda; Naoshi Nishida; Akihiro Yoshida; Tomoki Yamamoto; Takuya Matsubara; Masatoshi Kudo

doi:10.2169/internalmedicine.3270-23

Satoru Hagiwara, Koichi Nakagawa, Yoriaki Komeda, Naoshi Nishida, Akihiro Yoshida, Tomoki Yamamoto, Takuya Matsubara, Masatoshi Kudo

Author information

Satoru Hagiwara
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Koichi Nakagawa
Department of Dermatology, Saiseikai Tondabayashi Hospital, Japan
Yoriaki Komeda
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Naoshi Nishida
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Akihiro Yoshida
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Tomoki Yamamoto
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Takuya Matsubara
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan
Masatoshi Kudo
Department of Gastroenterology and Hepatology, Kindai University Faculty of Medicine, Japan

Keywords: Aneurysm, Hepatic focal nodular hyperplasia, Hereditary hemorrhagic telangiectasia, Rendu-Osler-Weber disease, Splenic artery, Vascular malformations

JOURNAL OPEN ACCESS Advance online publication

Article ID: 3270-23

DOI https://doi.org/10.2169/internalmedicine.3270-23

Details

Abstract

In October 2021, a 51-year-old woman developed a skin rash. Abdominal computed tomography revealed a large splenic artery aneurysm and an intrahepatic portovenous shunt. As her splenic artery aneurysm was at risk of rupture, she was referred to the Kindai University Hospital and underwent coiling surgery. In October 2023, approximately two years after she had been initially referred, contrast-enhanced ultrasound revealed findings suggestive of focal nodular hyperplasia. No reports have confirmed the occurrence of liver masses in patients with hereditary hemorrhagic telangiectasia, which is considered to be an interesting finding when investigating the mechanism of tumor development.

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