A Case of Idiopathic Pulmonary Hemosiderosis Associated with Emphysematous Change in an Adult Who Underwent Lung Transplantation

Kyoko Gocho; Kenya Sato; Keisuke Imasaka; Nobuyuki Hamanaka; Miki Takahashi; Kunihiko Shimizu; Tamiko Takemura

doi:10.2169/internalmedicine.5142-20

This article has now been updated. Please use the final version.

A Case of Idiopathic Pulmonary Hemosiderosis Associated with Emphysematous Change in an Adult Who Underwent Lung Transplantation

Kyoko Gocho, Kenya Sato, Keisuke Imasaka, Nobuyuki Hamanaka, Miki Takahashi, Kunihiko Shimizu, Tamiko Takemura

Author information

Keywords: idiopathic pulmonary hemosiderosis, peribronchiol hemosiderosis, emphysematous change, Ehlers-Danlos syndrome, lung transplantation

JOURNAL OPEN ACCESS Advance online publication

Article ID: 5142-20

DOI https://doi.org/10.2169/internalmedicine.5142-20

The final version of this article is now available: Vol. 60 (2021), No. 1 pp. 117-122

Details

Abstract

Idiopathic pulmonary hemosiderosis is characterized by repeated alveolar hemorrhaging. We herein report a 52-year-old Japanese woman who had shortness of breath, diffuse small nodules, thin-walled cysts, and bronchiolectasis. A surgical lung biopsy revealed peribronchial hemosiderosis, centrilobular emphysema, and fragile elastic fibers of the alveolar septa and small vessels. She ultimately underwent living-donor lung transplantation five years after the first visit.

Corresponding author

Register with J-STAGE for free!