抄録
Idiopathic restrictive cardiomyopathy (RCM) is rare. Even today little is understood of its etiology or under-lying mechanisms , and definitive diagnostic criteria are lacking. In this report, we describe a case of idiopathic RCM in a young Japanese woman who died while awaiting cardiac transplantation during the 5-year course of the disease. Rare pathologic findings of diffuse perimyocytic fibrosis were revealed at autopsy. (Jpn Circ J 1997; 61: 272 - 274)