Abstract
Hemophilia A is an X-linked hereditary disease. Pharyngolaryngeal hematomas associated with hemophilia sometimes cause airway stenosis, and require a tracheotomy. We herein report a patient who developed a pharyngolaryngeal hematoma who had type A hemophilia. He complained of dyspnea and throat pain following upper airway inflammation. In this case, factor replacement therapy, an antibiotic and steroids were rapidly administered, and this regimen proved to be very effective for treating the hematoma. His symptoms and the hematoma improved within a few days. We believe that factor replacement therapy and appropriate management of the airway are therefore very important for the successful treatment of this disease.