Abstract
Rhomboidosarcomas account for 15% of malignant childhood tumors. The head and neck region is one of the favorite sites of rhomboidosarcoma, followed by the limbs and trunk in 37% of cases of head and neck nuclear primary malignant tumors. However, rhomboidosarcoma of the nasopharynx is rare in the head and neck region. It generates from the nasopharyngeal wall. We herein present an example of a rhomboidosarcoma that was considered to have broadly progressed to the eustachian tubes, middle ear, middle cranial fossa, external auditory canal and temporal bone.
