急性感音難聴を発症した多発性海綿状血管腫例

抄録

We report a case of acute sensorineural hearing loss caused by multiple cavernous hemangiomas. The patient was a 38-year-old woman who presented to us with a history of sudden loss of hearing on the left side and left-sided tinnitus. After two weeks, both the symptoms improved, but a pure-tone audiometry revealed sensorineural hearing loss in the zone of scale-out on the left side. Initially, we suspected functional deafness, however, the patient was finally diagnosed as having retrocochlear deafness based on evaluation of the auditory brainstem response (ABR) following that of the distortion product optoacoustic emission (DPOAE). Furthermore, MRI revealed multiple cavernous hemangiomas, one of which was at the left cerebellopontine angle.

We conclude that objective auditory testing is very useful for evaluation of the hearing ability in patients with sensorineural hearing loss, but it is necessary to understand the characteristics of each test for an accurate interpretation of the results.