声門下狭窄を伴ったSweet病例

抄録

Sweet syndrome is characterized by fever, neutrophilia and painful skin lesions that appear mostly on the arms, neck, head and trunk. Sweet syndrome sometimes causes laryngopharyngeal lesions, and subglottic stenosis is very rare. We report a case of Sweet syndrome with subglottic stenosis.

The patient was a 69-year-old female who complained chiefly of fever, skin lesions and inspiratory stridor. She had fever and neck pain for 4 weeks prior to hospitalization. One or two weeks after the onset of symptoms, she developed painful erythema on her limbs. Her symptoms worsened, and inspiratory stridor appeared a few days before her visit to our hospital. A dermatologist at our hospital suspected Sweet syndrome based on the skin rash and consulted with us to examine the stridor. The patient’s subglottis was stenosed, and we conducted a tracheotomy. Steroid administration was very effective, and the airway narrowing improved. As of 10 months after her discharge from the hospital, the airway stenosis had not recurred; however, Sweet syndrome recurred 2 months ago, and the patient is presently receiving treatment.

Treatment for Sweet syndrome consists of corticosteroid medications, such as prednisone. Antibiotics have no effect on the disease. It is difficult to treat Sweet syndrome properly if the characteristic skin rash is missed. As in this case, Sweet syndrome can cause airway narrowing. Proper diagnosis and treatment are important.