Langerhans cell histiocytosis (LCH) is a relatively rare disease characterized by proliferation of abnormal Langerhans cells in various organs. We report the case of a young boy diagnosed as having LCH who initially presented with postauricular swelling.
A one-year and two-month-old boy with a swelling in the right postauricular region was referred to our clinic. CT revealed soft tissue densities with bone destruction in the right temporal bone, and MRI revealed contrast-enhancing lesions in the right temporal bone. The diagnosis of LCH was made by histopathological examination by needle biopsy specimens obtained under ultrasonographic guidance. Subsequently, systemic chemotherapy was administered, and remission was achieved. At present, 24 months later, the child remains in remission. Although LCH is a rare disease, it may occur first in the temporal bone, and this disease should be included in the differential diagnosis of refractory mastoid inflammation in children.
