We report a rare case with astrocytoma in the region of the bilateral cerebellopontine angle. The patient was a 33-year-old male who was diagnosed with neurofibromatosis 2 by clinical, audiovestibular and neuroradiological examination. However, the postoperative pathological diagnosis was consistent with fibrillary astrocytoma. Most gliomas in the posterior cranial fossa arise from the brainstem, and seldom originate in the vestibulocochlear nerve. Thus, we discuss the characteristics of glioma arising in the eighth cranial nerve and its association with neurofibromatosis 2.
