An inflammatory pseudotumor is one of the major neoplasm arising in the orbit. We reported a case of inflammatory pseudotumor of the orbit that was successfully treated. A 73-old-male was referred to our department with a complaint of swelling of the left eye lid. CT findings showed a tumor of the left orbit extending into the ethmoid sinus. Incisional biopsy was performed through the left maxillary sinus. Histologic examination demonstrated a non-specific inflammatory lesion with fibrous tissues and inflammatory cells. The pathologic diagnosis was benign pseudotumor. The patient was given steroid therapy (for 5 weeks) and radiotherapy (2Gy×10 days) which resulted in complete response at discharge. Steroid therapy was continued for 6 months after discharge. There has not been any recurrence of the tumor during more than 2 years follow up. Clinical manifestations, histopathologic findings and treatment of this lesion are discussed.
