Abstract
Human tail, a rare congenital "tail–like" anomaly, is usually attached to the sacrococcygeal skin. We report an extremely rare case of perianal tail in a 2–month–old boy. Physical examination and magnetic resonance imaging (MRI) showed no associated anomaly. The tail was resected without complications. Microscopically, it consisted mainly of fatty tissue, with nerve fibers and striated muscle fibers. The dermis showed smooth–muscle hyperplasia. This case is classified as a"caudal appendage" based on Harrison's classification and as a"true tail" based on Dao's and Lin's classification.