Japanese Journal of Cardiovascular Surgery
Online ISSN : 1883-4108
Print ISSN : 0285-1474
ISSN-L : 0285-1474
Case Reports
A Surgical Case of Mitral Regurgitation and Atrial Septal Defect with Myotonic Dystrophy
Mika IwazakiAyumu MasudaShunei KyoToshiyuki Katogi
Author information
JOURNAL FREE ACCESS

2009 Volume 38 Issue 2 Pages 119-122

Details
Abstract
Myotonic dystrophy (MyD) is a rare progressive multisystemic-inherited neuromuscular disease. It is often associated with cardiovascular disorders which require surgical procedures. However, it high sensitivity to anesthetic and neuromuscular blocking agents may result in respiratory complications. Myotonic dysorder due to hypothermia and conductive disorder following open-heart surgery are also risk-factor of perioperative management, thus open-heart surgery for MyD has rarely been reported. We describe the perioperative management for a MyD patient with an atrial septal defect (ASD) and mitral regurgitation (MR), who successfully underwent cardiac surgery. Minimally invasive cardiac surgery (MICS) with reverse-L-shaped partial sternotomy were useful method to minimize postoperative respiratory problems.
Content from these authors
© 2009 The Japanese Society for Cardiovascular Surgery
Previous article Next article
feedback
Top